Antiphospholipid syndrome presenting as isolated renal vein thrombosis: a case report and review of the literature.

Summary: Imagine a healthy 10-year-old girl suddenly getting a bad stomach ache, a fever, and blood in her pee. When doctors checked her, they found a large blood clot blocking the vein that drains her right kidney. After running some blood tests, they discovered she had a rare immune system problem called Antiphospholipid Syndrome (APS), which was caused by Lupus. Her body was making confusing signals that caused her blood to clot too easily.

Doctors quickly treated her with blood thinners to stop the clot from growing and medicine to lower her blood pressure. Even though the clot caused her right kidney to stop working, her left kidney stepped up and did the work of both! Four years later, she is doing great. She is growing normally, her kidney function is perfect, and she no longer even needs blood pressure medicine.